Surgical outcome of myelomeningocele repair associated with Chiari type II malformation

Keval Sanasiya; Deepak Joshi; Mehul Solanki

doi:10.53730/ijhs.v6nS6.12343

Surgical outcome of myelomeningocele repair associated with Chiari type II malformation

https://doi.org/10.53730/ijhs.v6nS6.12343

Authors

Keval Sanasiya Assistant Professor, Department of Neursurgery, Smt B.K Shah Medical Institute and Research Centre, Pipariya Vadodara
Deepak Joshi Assistant Professor, Department of Neursurgery, Smt B.K Shah Medical Institute and Research Centre, Pipariya Vadodara
Mehul Solanki
miissacc13@gmail.com
Resident, Department of Neursurgery, Smt B.K Shah Medical Institute and Research Centre, Pipariya Vadodara

Keywords:

Myelomeningocele (MMC), Arnold Chiari malformation II (ACM II), hydrocephalus (HCP), folic acid

Abstract

Introduction: Meningomyelocele, more commonly known as spina bifida (open) is a congenital malformation of the central nervous system and is associated with significant morbidity. Myelomeningocele is a commonly seen congenital birth defect in children. The most common associations with myelomeningocele are hydrocephalus and ACM Type 2. Folic acid deficiency and parental consanguinity appear to play a major part in this type of congenital defects. Objectives: To analyse the clinical profile and outcome of surgery in cases of myelomeningocele associated with Arnold Chiari malformation II and hydrocephalus. Methods: A Retrospective Cohort study was done starting from January 2015 to January 2019 in the Department of Neurosurgery at SBKS Medical College. Total 18 patients with Myelomeningocele associated with Arnold Chiari malformation II and Hydrocephalus were analysed and evaluated. Follow up of cases was done for a minimum period of 6 months. Results: Out of 18 total cases, the majority of cases, i.e., 76.8%, had myelomeningocele with Chiari II malformation and hydrocephalus. Ratio of females to males was 1.14. Prenatal folic acid supplementation was missed amongst 80% of the cases. 16.6% cases had positive parental consanguinity. Mortality was seen in 2 cases due to post operative complications. Myelomeningocele (MMC)

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Published

31-08-2022

How to Cite

Sanasiya, K., Joshi, D., & Solanki, M. (2022). Surgical outcome of myelomeningocele repair associated with Chiari type II malformation. International Journal of Health Sciences, 6(S6), 8347–8352. https://doi.org/10.53730/ijhs.v6nS6.12343

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Issue

Vol. 6 No. S6 (2022)

Section

Peer Review Articles

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