Frequency and outcomes of associated anomalies in anorectal malformation in children
Keywords:
anorectal malformation, anomalies, outcome, childrenAbstract
Background and Aim: Anorectal malformations (ARMs) are frequently occurring abnormalities in newborns. The occurrence of these issues is due to prenatal dysmorphogenesis affecting the cloaca and urorectum, leading to a significant medical concern. The present study aimed to determine the incidence and outcomes of associated abnormalities in Children with Anorectal Malformations. Patients and Methods: This retrospective case series study was conducted on 46 anorectal malformation children in the department of Pediatric Surgery, Mardan Medical Complex, Mardan - Pakistan from January 2021 to December 2022. Anorectal malformation children requiring surgical intervention were enrolled. Demographics details, anorectal malformations, specific types, and associated congenital anomalies were recorded. Results: Of the total 46 anorectal malformation children, there were 30 (65.2%) male and 16 (34.8%) females. A fistula was detected in 35 out of 46 cases, constituting 76.1% of the total cases examined. The prevailing type of fistula identified was rectourethral 34.3% (n=12), with rectovestibular fistula following closely at 31.4% (n=11). The most frequently occurring associated anomaly was cardiac, observed in 39.1% (n=18) of cases, followed by urological anomalies, which were present in 30.4% (n=14) of the cases. The present study found that anorectal malformation associated with functional outcomes mainly rely on the condition's severity.
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